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Tuberous sclerosis associated with giant bilateral bleeding angiomyolipomas

¹ *Departments of Internal Medicine,
² Radiology, and
³ Surgery, 251 Hellenic Air Force and Veterans General Hospital, Athens, Greece

Correspondence to:
Correspondence to:
Dr Anagnostopoulos;
gkanagnostopoulos@yahoo.gr

Keywords: tuberous sclerosis; agiomyolipomas

The first 150 words of the full text of this article appear below.

Tuberous sclerosis is a systemic disorder characterised by benign hamartomatous tumours that involve multiple organ systems. Angiomyolipomas are found in about two thirds of the kidneys of patients with tuberous sclerosis at necropsy.¹

A 29 year old woman with tuberous sclerosis presented with diffuse abdominal pain, gross haematuria, and hypotension. At the age of 22 the patient had been admitted to our hospital with acute upper abdominal pain and gross haematuria. Physical examination had revealed bilateral massive abdominal masses with no tenderness. Computed tomography had confirmed the presence of giant bilateral renal masses with the typical appearance of an angiomyolipoma, and a huge retroperitoneal haematoma extending to the pelvis and the left side of the abdomen (fig 1). After arterial embolisation, left radical nephrectomy was performed. The pathological diagnosis was angiomyolipoma without malignant findings, and the patient was discharged two weeks after the operation (fig 2).

View larger version (120K): [in this window] [in a new window]   Figure 1  Abdominal computed . . . [Full text of this article]